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Details of PSQ01739

ProSeqID PSQ01739
Family FD00183
Protein Name Paraplegin
UniProt ID Q3ULF4
Taxonomy Eukaryota-Metazoa-Chordata-Craniata-Vertebrata-Euteleostomi-Mammalia-Eutheria-Euarchontoglires-Glires-Rodentia-Myomorpha-Muroidea-Muridae-Murinae-Mus-Mus
Organisms Mus musculus (Mouse)
Prosequence Length (aa) 62
Functions ATP binding, ATP-dependent peptidase activity, metalloendopeptidase activity, zinc ion binding
Preproprotein Length (aa) 781
Alt Name Spastic paraplegia 7 protein
Gene Name Spg7
NCBI ID 10090
Cellular Localization axon cytoplasm, m-AAA complex, mitochondrial inner membrane, mitochondrial permeability transition pore complex, mitochondrion
Processes anterograde axonal transport, cell adhesion, cristae formation, mitochondrial fusion, mitochondrial outer membrane permeabilization involved in programmed cell death, mitochondrial protein processing, mitochondrion organization, protein-containing complex assembly, regulation of cell adhesion, regulation of mitochondrial membrane permeability
PubMed 19656850
Total Prosequence Length (aa) 62
Prosequence Location 44:105
Prosequence Sequence AARGTPVGPAAAGGHAPQSLLLRILTPSFEGISGLLLKQHIVPNAVRLWPLSGSTLYFNTSR
Preproprotein Sequence MAAALLLLRGLRPGPEPRPRRLWGLLSGRGPGLSSGAGARRPYAARGTPVGPAAAGGHAPQSLLLRILTPSFEGISGLLLKQHIVPNAVRLWPLSGSTLYFNTSRMKQKNKDNDKPKGKTPEDDEEEKRRKEREDQMYRERLRTLFIIALVMSLLNSLSTSGGSISWADFVNEMLAKGEVQRVQVVPESDVVEVYLHPGAVVFGRPRLALMYRMQVANIDKFEEKLRAAEDELNIESKDRIPVSYKRTGFFGNALYALGMTAVGLAILWYVFRLAGMTGREGGFSAFNQLKMARFTIVDGKTGKGVSFQDVAGMHEAKLEVREFVDYLKSPERFLQLGAKVPKGALLLGPPGCGKTLLAKAVATEAQVPFLAMAGPEFVEVIGGLGAARVRSLFKEARARAPCIVYIDEIDAVGKKRSTSMSGFSNTEEEQTLNQLLVEMDGMGTTDHVIVLASTNRADVLDNALMRPGRLDRHVFIDLPTLQERREIFEQHLKGLKLTQPSSFYSQRLAELTPGFSGADIANICNEAALHAAREGHTSVHTFNFEYAVERVIAGTAKKSKILSKEEQRVVAFHESGHALVGWLLEHTEAVMKVSIAPRTNAALGFSQMLPRDQYLFTKEQLFERMCMALGGRAAEAISFSRVTSGAQDDLRKVTRIAYSMVKQFGMAPSIGPVSFPEAQEGLMGIGRRPFSQGLQQMMDHEAKLLVAKAYRHTEKVLLDNLDKLQALANALLEKEVINYEDIEALIGPPPHGPKKMIAPQKWIDAEKERQASGEEEAPAP